Ornithine Carbamoyltransferase/OTC Rabbit mAb
产品介绍
This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also.
产品性质
产品特色
推荐稀释比 IHC:1/100-1/200
存储条件
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze/thaw cycles.
COA
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